{"entities":{"Q89214":{"pageid":79599,"ns":120,"title":"Item:Q89214","lastrevid":492244,"modified":"2026-08-15T15:47:12Z","type":"item","id":"Q89214","labels":{"mul":{"language":"mul","value":"ID_1810106678"},"pt-br":{"language":"pt-br","value":"Hemofilia B leve"},"en":{"language":"en","value":"Mild haemophilia B"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Hemofilia B leve \u00e9 uma forma de hemofilia B (veja este termo) caracterizada por uma defici\u00eancia leve de fator IX, levando a sangramento anormal como resultado de ferimentos menores ou subsequente a cirurgias ou extra\u00e7\u00f5es dent\u00e1rias. Hemofilia B leve responde por cerca de 30% de todos os casos de hemofilia B. A atividade biol\u00f3gica do fator IX encontra-se entre 5% e 40%. Hemorragias espont\u00e2neas n\u00e3o ocorrem. A transmiss\u00e3o \u00e9 recessiva ligada ao X, e o transtorno \u00e9 causado por muta\u00e7\u00f5es no gene F9 (Xq28), que codifica o fator IX da coagula\u00e7\u00e3o."},"en":{"language":"en","value":"Mild haemophilia B is a form of haemophilia B characterised by a small deficiency of factor IX leading to abnormal bleeding as a result of minor injuries, or following surgery or tooth extraction. Mild haemophilia B accounts for around 30% of all cases of haemophilia B. The biological activity of factor IX is between 5 and 40%. Spontaneous haemorrhages do not occur. Transmission is X-linked recessive and the disorder is caused by mutations in the F9 gene (Xq28) encoding coagulation factor IX."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"495c143a2bab823778498a836724eaefaae9c42a","datavalue":{"value":"https://id.who.int/icd/entity/1810106678","type":"string"},"datatype":"url"},"type":"statement","id":"Q89214$630DFEC6-590E-4290-AEA6-8889DBA487CD","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"590ce4f418460b0d92fec2a85eda4fa2910afab5","datavalue":{"value":"CID11:ID_1810106678","type":"string"},"datatype":"string"},"type":"statement","id":"Q89214$36DDFB46-AE30-42AF-89C3-22FA6675744D","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"fab18bb497eeb7d8b6cf934e3cefde47fadca59d","datavalue":{"value":"dki-india-ID_1810106678","type":"string"},"datatype":"string"},"type":"statement","id":"Q89214$3B9CC2E5-CC2E-48BB-A1A5-89E813E10987","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q89214$C7B744EC-48DF-4FCE-BDE7-B1BDF5F82C33","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q89214$99CAF103-DA72-40D2-B38D-9F7FDF84FBC6","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q89214$4D1AFBD0-DB9A-4880-BF39-F60AC9DA2D07","rank":"normal"}]},"sitelinks":{}}}}