{"entities":{"Q86040":{"pageid":76425,"ns":120,"title":"Item:Q86040","lastrevid":469124,"modified":"2026-08-15T11:24:19Z","type":"item","id":"Q86040","labels":{"mul":{"language":"mul","value":"ID_1665867595"},"pt-br":{"language":"pt-br","value":"Dentinog\u00eanese imperfeita tipo 1"},"en":{"language":"en","value":"Dentinogenesis imperfecta type 1"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Transtorno heredit\u00e1rio de desenvolvimento do dente, transmitido como tra\u00e7o autoss\u00f4mico dominante, e caracterizado por altera\u00e7\u00e3o da cor dos dentes, variando de azul moderadamente escuro a amarronzada, dentina mal formada com conte\u00fado mineral anormalmente baixo, oblitera\u00e7\u00e3o do canal pulpar e esmalte normal. Os dentes geralmente se desgastam rapidamente, restando tocos curtos e marrons. Tamb\u00e9m chamado de d. heredit\u00e1ria hipopl\u00e1sica, s\u00edndrome de Capdepont-Hodge, s\u00edndrome de Capdepont, s\u00edndrome de Fargin-Fayelle, dentes escuros heredit\u00e1rios, dentina opalescente heredit\u00e1ria, dentes opalescentes heredit\u00e1rios, odontog\u00eanese imperfeita, s\u00edndrome de Stainton-Capdepont e s\u00edndrome de Stainton. O tipo 1 est\u00e1 relacionado \u00e0 cementog\u00eanese imperfeita e \u00e0 osteog\u00eanese imperfeita."},"en":{"language":"en","value":"A hereditary disorder of tooth development, transmitted as an autosomal dominant trait, and characterised by discoloration of the teeth, ranging from dusky blue to brownish, poorly formed dentin with an abnormally low mineral content, obliteration of the pulp canal, and normal enamel. The teeth usually wear down rapidly, leaving short, brown stumps. Called also d. hypoplastic hereditaria, Capdepont-Hodge syndrome, Capdepont\u2019s syndrome, Fargin-Fayelle syndrome, hereditary dark teeth, hereditary opalescent dentin, hereditary opalescent teeth, odontogenesis imperfect, Stainton-Capdepont syndrome, and Stainton syndrome. Type 1 is related to cementogenesis imperfecta and osteogenesia imperfect."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"33ba88344a32c2dcda74ba4b75ae513e852c996a","datavalue":{"value":"https://id.who.int/icd/entity/1665867595","type":"string"},"datatype":"url"},"type":"statement","id":"Q86040$DC61DB02-34F6-4C86-BB6C-C5B63BBB65EA","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"f46dfa41212a6b7a562a46bc73fb588a276b0687","datavalue":{"value":"CID11:ID_1665867595","type":"string"},"datatype":"string"},"type":"statement","id":"Q86040$4AEEBECC-3454-411F-9CF2-0ED858ED7290","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"db30af6207382f79dcd58ec7190b08e26297e294","datavalue":{"value":"dki-india-ID_1665867595","type":"string"},"datatype":"string"},"type":"statement","id":"Q86040$91A092B9-A3E3-4905-BEC3-71DA176532B6","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q86040$416E9F46-B95F-4DB0-8A89-46633CC5D786","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q86040$C6BF2E64-3BDB-456B-B4FB-BB265488038B","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q86040$12429598-1F21-4575-B575-38169862636B","rank":"normal"}]},"sitelinks":{}}}}