{"entities":{"Q84891":{"pageid":75276,"ns":120,"title":"Item:Q84891","lastrevid":460775,"modified":"2026-08-15T10:15:07Z","type":"item","id":"Q84891","labels":{"mul":{"language":"mul","value":"ID_170763135"},"pt-br":{"language":"pt-br","value":"S\u00edndrome de disgenesia cerebral - neuropatia - ictiose - ceratodermia"},"en":{"language":"en","value":"Cerebral dysgenesis \u2013 neuropathy \u2013 ichthyosis \u2013 keratoderma syndrome"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A s\u00edndrome CEDNIK \u00e9 uma s\u00edndrome neurocut\u00e2nea caracterizada por graves anormalidades de desenvolvimento do sistema nervoso e diferencia\u00e7\u00e3o aberrante da epiderme. Clinicamente, \u00e9 definida por uma constela\u00e7\u00e3o \u00fanica de sinais cl\u00ednicos descritos com a sigla CEDNIK: Cerebral Disgenesia, Neuropatia, Ictiose, e ceratodermia palmoplantar."},"en":{"language":"en","value":"CEDNIK syndrome is a neurocutaneous syndrome characterised by severe developmental abnormalities of the nervous system and aberrant differentiation of the epidermis. Clinically, it is defined by a unique constellation of clinical signs described with the acronym CEDNIK: Cerebral Dysgenesis, Neuropathy, Ichthyosis, and palmoplantar Keratoderma."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"a457a663fb4036b66d06940b27f3f83eda09c2fa","datavalue":{"value":"https://id.who.int/icd/entity/170763135","type":"string"},"datatype":"url"},"type":"statement","id":"Q84891$B43AA23E-E815-4D37-BFC8-C42ECCFCFCD2","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"63a5efc6ab262526926b7a4a29fa9816be2765ad","datavalue":{"value":"CID11:ID_170763135","type":"string"},"datatype":"string"},"type":"statement","id":"Q84891$AD62BEEE-8C23-46C5-A791-D1B9FBF4E11F","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"41a8cff11dc3b27ede05b5d9670bc834f342b9bb","datavalue":{"value":"dki-india-ID_170763135","type":"string"},"datatype":"string"},"type":"statement","id":"Q84891$AA478B22-7A89-4830-B5F2-AAE7F36CB25D","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q84891$4AA59EF8-26BD-4876-8607-BC5966BA7FFE","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q84891$886CFFD1-6E3B-4708-8F0B-81041768235C","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q84891$6883F9B6-761F-4205-AB61-5BA7E6B15544","rank":"normal"}]},"sitelinks":{}}}}