{"entities":{"Q84779":{"pageid":75164,"ns":120,"title":"Item:Q84779","lastrevid":459954,"modified":"2026-08-15T10:07:58Z","type":"item","id":"Q84779","labels":{"mul":{"language":"mul","value":"ID_331119306"},"pt-br":{"language":"pt-br","value":"Doen\u00e7a de dep\u00f3sito de glicog\u00eanio por defici\u00eancia de LAMP-2"},"en":{"language":"en","value":"Glycogen storage disease due to LAMP-2 deficiency"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Doen\u00e7a de dep\u00f3sito de glicog\u00eanio devido a defici\u00eancia de LAMP-2 (Prote\u00edna 2 de Membrana Associada ao Lisossoma) \u00e9 uma doen\u00e7a de dep\u00f3sito de glicog\u00eanio lisossomal caracterizada por miocardiopatia grave e v\u00e1rios graus de fraqueza muscular, frequentemente associada com comprometimento intelectual."},"en":{"language":"en","value":"Glycogen storage disease due to LAMP-2 (Lysosomal-Associated Membrane Protein 2) deficiency is a lysosomal glycogen storage disease characterised by severe cardiomyopathy and variable degrees of muscle weakness, frequently associated with intellectual deficit."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"2578e7c5abc5a5e5bec3e09373edbe7c442d329e","datavalue":{"value":"https://id.who.int/icd/entity/331119306","type":"string"},"datatype":"url"},"type":"statement","id":"Q84779$B26D48CE-C44B-4C8F-B35A-43717915045E","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"04bb52661e66d8f3e8650550d59dfc3128cb5194","datavalue":{"value":"CID11:ID_331119306","type":"string"},"datatype":"string"},"type":"statement","id":"Q84779$818BEB02-EFEC-432D-832C-281F874C142F","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"2d5240e72478c6888b362249f04c597d6d28d1c0","datavalue":{"value":"dki-india-ID_331119306","type":"string"},"datatype":"string"},"type":"statement","id":"Q84779$00C97F9C-295E-4919-A50D-3CC865C52BF9","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q84779$BABA86A0-F65F-4E09-8670-3ED5587252E8","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q84779$77E5F1B7-33A2-4BAD-BEEB-826F3F3AA25A","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q84779$56208854-72AD-497A-A556-7D0E38815A76","rank":"normal"}]},"sitelinks":{}}}}