{"entities":{"Q46709":{"pageid":37080,"ns":120,"title":"Item:Q46709","lastrevid":183592,"modified":"2026-08-13T15:29:29Z","type":"item","id":"Q46709","labels":{"mul":{"language":"mul","value":"LD2F.12"},"pt-br":{"language":"pt-br","value":"Sirenomelia"},"en":{"language":"en","value":"Sirenomelia"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Sirenomelia \u00e9 uma malforma\u00e7\u00e3o letal rara caracterizada por graves anomalias da parte caudal do feto que incluem um \u00fanico membro inferior, com v\u00e1rios graus de envolvimento variando desde um \u00fanico ou dois f\u00eamures separados no mesmo eixo de pele, presen\u00e7a de dois p\u00e9s (\"sereia\" simp\u00f3dica) ou um p\u00e9 (\"sereia\" monop\u00f3dica), at\u00e9 aus\u00eancia de ambos os p\u00e9s (\"sereia\" ectrom\u00e9lica). Anomalias urogenitais tamb\u00e9m est\u00e3o presentes e incluem agenesia renal bilateral, aus\u00eancia de via de sa\u00edda e aus\u00eancia de genit\u00e1lia externa. \u00c2nus imperfurado e agenesia sacrococc\u00edgea tamb\u00e9m foram relatados. Juntas, essas malforma\u00e7\u00f5es constituem a forma extrema da sequ\u00eancia de regress\u00e3o caudal."},"en":{"language":"en","value":"Sirenomelia is a rare lethal malformation characterised by severe anomalies of the caudal part of the fetus that include a single lower limb, with various degrees of involvement ranging from single to separate femurs in the same skin shaft, presence of two feet (sympode mermaid) or one foot (monopode mermaid), to absence of both feet (ectromelic mermaid). Urogenital anomalies are also present and include bilateral renal agenesis, absence of outflow tract and absence of external genitalia. Imperforate anus and sacro-coccygeal agenesis have also been reported. Together these malformations comprise the extreme form of the caudal regression sequence."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"8dbad258659c71099c0812e71486d097bc54baf0","datavalue":{"value":"https://id.who.int/icd/entity/473306797","type":"string"},"datatype":"url"},"type":"statement","id":"Q46709$FE89FECF-9C1D-461A-96A1-8A502E404D73","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"4bad5c237b8888a0da7ca1e91a966480c0591ca5","datavalue":{"value":"CID11:LD2F.12","type":"string"},"datatype":"string"},"type":"statement","id":"Q46709$C5906D82-33C9-4926-9221-0A96D4F75167","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"eaf775e3df675be5f81bbdd2acb48eb4d3010e22","datavalue":{"value":"dki-india-LD2F.12","type":"string"},"datatype":"string"},"type":"statement","id":"Q46709$0B506673-AB28-4860-ABEB-B03D5325D383","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q46709$6202F04C-1B68-4775-BB75-0B6F9AADB7CF","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q46709$A2927D1D-4BDD-4E77-BB4B-9DE567184FC6","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q46709$F1F11FA9-29C0-42AA-8436-720E1B87953E","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"8fe7cda765cdedc2ec2319c6b5943feb0659c921","datavalue":{"value":{"entity-type":"item","numeric-id":872,"id":"Q872"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q46709$5ED051F9-EFC5-4B4E-ACB9-ABEC66DB3ABE","rank":"normal"}]},"sitelinks":{}}}}