{"entities":{"Q46596":{"pageid":36967,"ns":120,"title":"Item:Q46596","lastrevid":182555,"modified":"2026-08-13T15:17:00Z","type":"item","id":"Q46596","labels":{"mul":{"language":"mul","value":"LD24.B0"},"pt-br":{"language":"pt-br","value":"S\u00edndrome de costela curta - polidactilia"},"en":{"language":"en","value":"Short rib-polydactyly syndrome"}},"descriptions":{"pt-br":{"language":"pt-br","value":"As s\u00edndromes de costela curta-polidactilia s\u00e3o um grupo de malforma\u00e7\u00f5es \u00f3sseas caracterizadas por um t\u00f3rax estreito e polidactilia (geralmente pr\u00e9-axial). A preval\u00eancia como grupo \u00e9 desconhecida. O grupo \u00e9 heterog\u00eaneo e inclui a s\u00edndrome de Jeune e a s\u00edndrome de Ellis-Van Creveld, nenhuma das quais \u00e9 letal, juntamente com condrodisplasias letais: Saldino-Noonan (tipo 1), Majewski (tipo 2), Verma-Naumoff (tipo 3) e Beemer-Langer (tipo 4)."},"en":{"language":"en","value":"Short rib-polydactyly syndromes are a group of bone malformations characterised by a narrow thorax and polydactyly (usually preaxial). Prevalence as a group is unknown. The group is heterogeneous and includes Jeune syndrome and Ellis-Van Creveld syndrome, neither of which are lethal, together with lethal chondrodysplasias: Saldino-Noonan (type 1), Majewski (type 2), Verma-Naumoff (type 3) and Beemer-Langer (type 4)."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"f97fdd2d318a339c15ce6f43676a44eae2cd7908","datavalue":{"value":"https://id.who.int/icd/entity/960900212","type":"string"},"datatype":"url"},"type":"statement","id":"Q46596$F0D8AE7D-6841-416C-879D-EEC5DA342279","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"ddac6ead5411331d08c9921e54e08158e6e39baa","datavalue":{"value":"CID11:LD24.B0","type":"string"},"datatype":"string"},"type":"statement","id":"Q46596$EE5B14B0-6DA7-487B-837E-1C2A69C00079","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"bcf44cb5aba3e61ad51f18a1a1f74256056597ac","datavalue":{"value":"dki-india-LD24.B0","type":"string"},"datatype":"string"},"type":"statement","id":"Q46596$2F9A15E3-F394-4F40-88C4-69E836C371E0","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q46596$72329BB6-3F0C-437A-BAF7-1E010B9DAEE3","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q46596$1A9B8658-A2E5-432C-9A49-B90D63BEEEA9","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q46596$700D2F46-24E8-4277-AD53-66DD84F055F6","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"60d136b2c8c1810c8e6df65b95c0a952f405db42","datavalue":{"value":{"entity-type":"item","numeric-id":772,"id":"Q772"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q46596$E365727B-E39F-4992-9754-41B4E302CF54","rank":"normal"}]},"sitelinks":{}}}}