{"entities":{"Q46319":{"pageid":36690,"ns":120,"title":"Item:Q46319","lastrevid":180082,"modified":"2026-08-13T14:49:20Z","type":"item","id":"Q46319","labels":{"mul":{"language":"mul","value":"LB13.0"},"pt-br":{"language":"pt-br","value":"Estenose hipertr\u00f3fica cong\u00eanita do piloro"},"en":{"language":"en","value":"Congenital hypertrophic pyloric stenosis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Malforma\u00e7\u00e3o cong\u00eanita n\u00e3o incomum do est\u00f4mago de causa desconhecida, na qual h\u00e1 hipertrofia e hiperplasia do m\u00fasculo circular do piloro. Sintomas de obstru\u00e7\u00e3o de via de sa\u00edda g\u00e1strica geralmente aparecem entre a terceira e a sexta semanas de vida. A anomalia se manifesta por v\u00f4mitos intermitentes (que aumentam de frequ\u00eancia e se transformam em v\u00f4mitos em jato), regurgita\u00e7\u00e3o, perda de peso, desidrata\u00e7\u00e3o, desequil\u00edbrio eletrol\u00edtico, \u00e0s vezes uma pequena massa pil\u00f3rica palp\u00e1vel e contra\u00e7\u00f5es perist\u00e1lticas vis\u00edveis no epig\u00e1strio; tamb\u00e9m pode haver icter\u00edcia. Alguns casos parecem ter origem familial (possivelmente de heran\u00e7a autoss\u00f4mica dominante)."},"en":{"language":"en","value":"A not uncommon congenital malformation of the stomach of unknown cause in which there is hypertrophy and hyperplasia of the circular muscle of the pylorus. Symptoms of gastric outlet obstruction usually appear between the third and sixth weeks of life. The anomaly is manifested by intermittent vomiting (which increases in frequency and becomes projectile), regurgitation, weight loss, dehydration, electrolyte imbalance, sometimes a small palpable pyloric mass, and visible peristaltic contractions across the epigastrium; there may also be jaundice. Some cases appear to be familial (possibly of autosomal dominant inheritance)."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"a3f54f4b14bc67b5110f9588c547829bf96fdcc2","datavalue":{"value":"https://id.who.int/icd/entity/224753192","type":"string"},"datatype":"url"},"type":"statement","id":"Q46319$F467ACEE-9C3A-4560-A7F0-022973ECF43A","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"542566732c458b08b74c78464f5a1157596062c8","datavalue":{"value":"CID11:LB13.0","type":"string"},"datatype":"string"},"type":"statement","id":"Q46319$B319A778-28C7-4075-886B-D860030007C4","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"0e3331eb2ca686f468615b10db5daac74b0d9f17","datavalue":{"value":"dki-india-LB13.0","type":"string"},"datatype":"string"},"type":"statement","id":"Q46319$85D701D7-4FD4-47D5-9F94-6CFDF6BAB874","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q46319$13A88115-919D-443F-8D70-80DB69F80E7B","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q46319$B1C7179E-4A18-4E77-A964-33035C32E186","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q46319$50565A69-9777-4395-B703-BFE143F1676E","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"79dc377cca515431582686380f5dda9cac55d8d7","datavalue":{"value":{"entity-type":"item","numeric-id":22033,"id":"Q22033"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q46319$ED8A5862-C45A-42E1-9100-3EE317A49C10","rank":"normal"}]},"sitelinks":{}}}}