{"entities":{"Q44617":{"pageid":34985,"ns":120,"title":"Item:Q44617","lastrevid":165203,"modified":"2026-08-13T12:10:12Z","type":"item","id":"Q44617","labels":{"mul":{"language":"mul","value":"FB82.3"},"pt-br":{"language":"pt-br","value":"Policondrite recidivante"},"en":{"language":"en","value":"Relapsing polychondritis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A policondrite recidivante \u00e9 uma doen\u00e7a inflamat\u00f3ria multissist\u00eamica de etologia desconhecida que acomete a cartilagem. \u00c9 caracterizada por manifesta\u00e7\u00f5es inflamat\u00f3rias intermitentes ou flutuantes, devidas a inflama\u00e7\u00e3o nas estruturas cartilaginosas, resultando em dano e destrui\u00e7\u00e3o teciduais. Condrite das cartilagens auricular, nasal e traqueal predominam nessa doen\u00e7a, o que sugere uma resposta inflamat\u00f3ria a ant\u00edgenos teciduais espec\u00edficos, como o col\u00e1geno do tipo II e a prote\u00edna de matriz cartilaginosa (matrilin-1). Em aproximadamente um ter\u00e7o dos pacientes, a PR est\u00e1 associada a vasculite (desde vasculite leucocitocl\u00e1stica cut\u00e2nea isolada at\u00e9 poliangeite sist\u00eamica) e doen\u00e7as reum\u00e1ticas autoimunes (principalmente a artrite reumatoide e o l\u00fapus eritematoso sist\u00eamico). Neoplasias hematol\u00f3gicas malignas, transtornos gastrointestinais e doen\u00e7as end\u00f3crinas podem ocorrer. A avalia\u00e7\u00e3o funcional e anat\u00f4mica para doen\u00e7as de vias a\u00e9reas superiores e inferiores \u00e9 essencial na avalia\u00e7\u00e3o e manejo desta doen\u00e7a."},"en":{"language":"en","value":"Relapsing polychondritis is a multisystem inflammatory disease of unknown aetiology affecting the cartilage. The disease is characterised by intermittent or fluctuant inflammatory manifestations due to inflammation of the cartilaginous structures, resulting in tissue damage and tissue destruction. Chondritis of auricular, nasal, tracheal cartilage predominates in this disease, suggesting response to tissue-specific antigens such as collagen II and cartilage matrix protein (matrillin-1). In about one third of patients, RP is associated with vasculitis (from isolated cutaneous leucocytoclastic vasculitis to systemic polyangiitis) and autoimmune rheumatic diseases (mainly rheumatoid arthritis and systemic lupus erythematosus). Haematological malignant diseases, gastrointestinal disorders and endocrine diseases may also occur. Functional and anatomical evaluation for upper and lower airway disease is essential in evaluation and management of the disease."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"131e3e277291d7c86da80423332f42b916d0811f","datavalue":{"value":"https://id.who.int/icd/entity/1412888287","type":"string"},"datatype":"url"},"type":"statement","id":"Q44617$A700ABAA-8A1F-46D9-AEE1-54AD61829941","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"fbd199a252f55b8df43407db39cb2dd883972a2f","datavalue":{"value":"CID11:FB82.3","type":"string"},"datatype":"string"},"type":"statement","id":"Q44617$54141CAC-E6B4-45F7-B369-2A806EB5425E","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"a79d40ff0b29f24550eba047acea20122cb9444e","datavalue":{"value":"dki-india-FB82.3","type":"string"},"datatype":"string"},"type":"statement","id":"Q44617$A174542C-E6A5-4823-9E64-4E1A35349E40","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q44617$932EAA57-777F-4182-A0B8-159E44830FEC","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q44617$0EECAC44-FBE9-4B2C-AF65-3B45F55E9B2A","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q44617$337277E4-2957-4B7B-B3BE-6C37E690775A","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"47904d9a2b5423e255cf091fcc1383d448095258","datavalue":{"value":{"entity-type":"item","numeric-id":20298,"id":"Q20298"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q44617$34BC264E-1215-4249-B1FD-01A229F08E2D","rank":"normal"}]},"sitelinks":{}}}}