{"entities":{"Q42951":{"pageid":33319,"ns":120,"title":"Item:Q42951","lastrevid":150694,"modified":"2026-08-13T09:43:17Z","type":"item","id":"Q42951","labels":{"mul":{"language":"mul","value":"CB07.1"},"pt-br":{"language":"pt-br","value":"Linfangioleiomiomatose espor\u00e1dica"},"en":{"language":"en","value":"Sporadic lymphangioleiomyomatosis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Doen\u00e7a pulmonar rara que resulta na prolifera\u00e7\u00e3o de crescimento desordenado de m\u00fasculo liso (leiomioma) nos pulm\u00f5es inteiros, nos bronqu\u00edolos, septos alveolares, espa\u00e7os perivasculares e linf\u00e1ticos, levando \u00e0 obstru\u00e7\u00e3o de pequenas vias a\u00e9reas (com forma\u00e7\u00e3o de cistos e de pneumot\u00f3rax) e dos linf\u00e1ticos (levando a derrame pleural quiloso). A LAM ocorre de forma espor\u00e1dica, afeta apenas mulheres, geralmente em idade reprodutiva; LAM ocorre tamb\u00e9m em pacientes que t\u00eam esclerose tuberosa."},"en":{"language":"en","value":"This is a rare lung disease that results in a proliferation of disorderly smooth muscle growth (leiomyoma) throughout the lungs, in the bronchioles, alveolar septa, perivascular spaces, and lymphatics, resulting in the obstruction of small airways (leading to pulmonary cyst formation and pneumothorax) and lymphatics (leading to chylous pleural effusion). LAM occurs in a sporadic form, which affects only females, usually of childbearing age; LAM also occurs in patients who have tuberous sclerosis."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"5a0f889ab00761d876c4ac21acf3205bd6a5b040","datavalue":{"value":"https://id.who.int/icd/entity/1251780231","type":"string"},"datatype":"url"},"type":"statement","id":"Q42951$2E9BEA36-E0BE-4803-847C-F288E5802B28","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"315782ade2f369e4caaaca0ffb0659e5c5b4897b","datavalue":{"value":"CID11:CB07.1","type":"string"},"datatype":"string"},"type":"statement","id":"Q42951$1C75E1B3-5C9F-490D-987D-3BCF517708C5","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"601b194c9ffc6f91791e3eaf6e8298f5b295af60","datavalue":{"value":"dki-india-CB07.1","type":"string"},"datatype":"string"},"type":"statement","id":"Q42951$D4FAEAB1-E9A7-46C1-90F0-8FB725792D94","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q42951$0D1BF479-3E1E-49BC-9109-DC3786DDE9E7","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q42951$7094DEF4-BBE5-48DA-90EF-4FE49082E6BB","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q42951$AE722253-60B7-4CDB-AD0D-1DDD19161BB7","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"650f08651bdaf59448369e90a98ac51615f4d99e","datavalue":{"value":{"entity-type":"item","numeric-id":18778,"id":"Q18778"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q42951$C9C3BD93-09ED-41C1-ABCE-38F5E375AFE5","rank":"normal"}]},"sitelinks":{}}}}