{"entities":{"Q41286":{"pageid":31654,"ns":120,"title":"Item:Q41286","lastrevid":136842,"modified":"2026-08-13T07:24:11Z","type":"item","id":"Q41286","labels":{"mul":{"language":"mul","value":"7A20.0"},"pt-br":{"language":"pt-br","value":"Narcolepsia tipo 1"},"en":{"language":"en","value":"Narcolepsy, Type 1"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Narcolepsia do Tipo 1 \u00e9 um transtorno de sonol\u00eancia excessiva devido \u00e0 defici\u00eancia de sinaliza\u00e7\u00e3o da hipocretina hipotal\u00e2mica (orexina). Al\u00e9m dos per\u00edodos di\u00e1rios de necessidade incontrol\u00e1vel de dormir ou lapsos de sono diurnos, a narcolepsia do tipo 1 \u00e9 caracterizada por sintomas de dissocia\u00e7\u00e3o do sono REM, mais importantemente a cataplexia. Cataplexia \u00e9 a perda s\u00fabita e incontrol\u00e1vel do t\u00f4nus muscular surgindo durante a vig\u00edlia que \u00e9 tipicamente desencadeada por uma emo\u00e7\u00e3o forte, como excita\u00e7\u00e3o ou risada. Embora a cataplexia seja um sintoma patognom\u00f4nico da narcolepsia do tipo 1, ela pode n\u00e3o se manifestar at\u00e9 anos depois do in\u00edcio da sonol\u00eancia. Em tais casos, o diagn\u00f3stico de narcolepsia do tipo 1 pode ser feito baseado nos n\u00edveis de hipocretina no l\u00edquido cefalorraquidiano (LCR) < 110 picogramas por mililitro. Epis\u00f3dios de paralisia do sono e alucina\u00e7\u00f5es hipnag\u00f3gicas ou hipnop\u00f4mpicas tamb\u00e9m podem estar presentes. O transtorno n\u00e3o \u00e9 atribu\u00edvel a uma doen\u00e7a do sistema nervoso ou outra condi\u00e7\u00e3o cl\u00ednica._x000D_ _x000D_ Nota: um diagn\u00f3stico definitivo requer per\u00edodos di\u00e1rios de necessidade irreprim\u00edvel de dormir ou lapsos diurnos de sono somado a ou: a) cataplexia e teste das lat\u00eancias m\u00faltiplas do sono/ polissonografia (TMLS/PSG) com achados caracter\u00edsticos de narcolepsia; ou b) defici\u00eancia demonstrada de hipocretina no LCR."},"en":{"language":"en","value":"Type 1 narcolepsy is a disorder of excessive sleepiness due to a deficiency of hypothalamic hypocretin (orexin) signaling. In addition to daily periods of irrepressible need to sleep or daytime lapses into sleep, type 1 narcolepsy is characterised by symptoms of REM sleep dissociation, most importantly cataplexy. Cataplexy is a sudden and uncontrollable loss of muscle tone arising during wakefulness that is typically triggered by a strong emotion, such as excitement or laughter. Although cataplexy is a pathognomonic symptom of type 1 narcolepsy, it may not manifest until years following onset of the sleepiness. In such cases, a diagnosis of narcolepsy, type 1 may be made based on cerebrospinal fluid (CSF)-hypocretin levels < 110 picograms per milliliter. Episodes of sleep paralysis and hypnagogic or hypnopompic hallucinations may also be present. The disorder is not attributable to a disease of the nervous system or other medical condition. Note: A definitive diagnosis requires daily periods of irrepressible need to sleep or daytime lapses into sleep plus either: a) cataplexy and multiple sleep latency test/polysomnography (MSLT/PSG) findings characteristic of narcolepsy; or b) demonstrated CSF hypocretin deficiency."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"811845fb88edc40a5015311265a8a162ae343e63","datavalue":{"value":"https://id.who.int/icd/entity/1851015159","type":"string"},"datatype":"url"},"type":"statement","id":"Q41286$2E49C580-2653-46DC-9CEA-23AEBC1C7C73","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"8297891c92077534991cda5571ea440489387ce3","datavalue":{"value":"CID11:7A20.0","type":"string"},"datatype":"string"},"type":"statement","id":"Q41286$F75CE940-FAA7-447B-80C0-036FE7837082","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"d6734510eb03dc2f4ed3b8c0f2a602883da027c1","datavalue":{"value":"dki-india-7A20.0","type":"string"},"datatype":"string"},"type":"statement","id":"Q41286$EAA86179-F517-46E5-9C20-6CD8D67468D7","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q41286$85A810F5-9C3C-4A9A-9C6A-AF02723450D1","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q41286$72D8738B-2E1E-4571-998D-E837240AA4A2","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q41286$15CF0E9C-6439-47D1-B5F6-FC1F10AFE36C","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"d19b0239137ba4256baadb460c99055b602177c0","datavalue":{"value":{"entity-type":"item","numeric-id":17086,"id":"Q17086"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q41286$91BCE8B3-72C1-4DA0-82B2-D8A2ED9B9D00","rank":"normal"}]},"sitelinks":{}}}}