{"entities":{"Q41170":{"pageid":31538,"ns":120,"title":"Item:Q41170","lastrevid":135803,"modified":"2026-08-13T07:13:53Z","type":"item","id":"Q41170","labels":{"mul":{"language":"mul","value":"8A44.2"},"pt-br":{"language":"pt-br","value":"Doen\u00e7a de Alexander"},"en":{"language":"en","value":"Alexander disease"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Doen\u00e7a de Alexander \u00e9 um transtorno neurodegenerativo que abrange diferentes formas cl\u00ednicas. A forma infantil (do nascimento aos 2 anos), a mais comum, \u00e9 caracterizada por in\u00edcio precoce e evolu\u00e7\u00e3o grave com megalencefalia (algumas vezes hidrocefalia), atraso do desenvolvimento psicomotor ou decl\u00ednio cognitivo, sinais piramidais, ataxia e crises convulsivas. A forma juvenil inicia-se na fase escolar da crian\u00e7a, e se associa a paraplegia esp\u00e1stica e sinais bulbares pogressivos. A forma adulta \u00e9 heterog\u00eanea e de d\u00edficil diagn\u00f3stico."},"en":{"language":"en","value":"Alexander's disease is a neurodegenerative disorder encompassing different clinical forms: the infantile form (birth to 2 years), the most common, is characterised by its early onset and severe evolution with progressive megalencephaly (sometimes hydrocephaly), retarded psychomotor development or mental deterioration, pyramidal signs, ataxia and convulsive seizures. The juvenile forms start in school-aged children and associate spastic paraplegia and progressive bulbar signs. Adult forms are heterogeneous and difficult to diagnose."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"5f21f66bc4f28eb7db5bae8756735c4d132f2482","datavalue":{"value":"https://id.who.int/icd/entity/2023359698","type":"string"},"datatype":"url"},"type":"statement","id":"Q41170$9898F942-AB31-43ED-9735-67DBD64111CC","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"781626b65a99a6a0abf42b0631d61946dfc206d9","datavalue":{"value":"CID11:8A44.2","type":"string"},"datatype":"string"},"type":"statement","id":"Q41170$5B4729BF-3BAF-4570-8CEC-D9BEC091E81A","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"b69f970c52b7f4c0e75043a7d61b7002d3cc5592","datavalue":{"value":"dki-india-8A44.2","type":"string"},"datatype":"string"},"type":"statement","id":"Q41170$4198CB73-51F5-48C1-BFBA-9B8A3AAE2EAB","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q41170$2C0FC114-F06F-4B4A-8E27-18172FEB81C2","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q41170$8DC8ABDA-9FF1-42F9-AF95-877DDA1D41AA","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q41170$CEAD67B2-2869-4387-9B25-B8393D2E3702","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"3c96e0a0eb81fb23e7b4b50212df27e93a90c409","datavalue":{"value":{"entity-type":"item","numeric-id":41169,"id":"Q41169"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q41170$EA6A6A90-D07B-4E88-84F2-42335EF214A6","rank":"normal"}]},"sitelinks":{}}}}