{"entities":{"Q41050":{"pageid":31418,"ns":120,"title":"Item:Q41050","lastrevid":134924,"modified":"2026-08-13T07:06:20Z","type":"item","id":"Q41050","labels":{"mul":{"language":"mul","value":"8B60.6"},"pt-br":{"language":"pt-br","value":"Amiotrofia monom\u00e9lica"},"en":{"language":"en","value":"Monomelic amyotrophy"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Atrofia e fraqueza restritas a um membro superior ou inferior, in\u00edcio na segunda ou terceira d\u00e9cada, predomin\u00e2ncia do sexo masculino e ocorr\u00eancia espor\u00e1dica s\u00e3o aspectos caracter\u00edsticos da atrofia monom\u00e9lica (AM). Outras caracter\u00edsticas t\u00edpicas incluem: in\u00edcio insidioso de sinais do neur\u00f4nio motor inferior devido a envolvimento das c\u00e9lulas do corno anterior, aus\u00eancia de sinais do neur\u00f4nio motor superior, progress\u00e3o lenta seguida de estabiliza\u00e7\u00e3o em alguns anos e curso benigno da doen\u00e7a sintom\u00e1tica. AM \u00e9 particularmente prevalente na \u00c1sia, embora seja encontrado em todo o mundo."},"en":{"language":"en","value":"Atrophy and weakness restricted to one upper or lower limb, onset in the second or third decade, male predominance, and sporadic occurrence are characteristic features of MMA. Other typical features include: insidious onset of lower motor neuron signs due to anterior horn cell involvement, absence of upper motor neuron signs, slow progression followed by stabilization within a few years,, and a benign symptomatic disease course. MMA is particularly prevalent in Asia although it is encountered worldwide."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"ec895ea93859f8394e08942f472e7497329580e1","datavalue":{"value":"https://id.who.int/icd/entity/2090347823","type":"string"},"datatype":"url"},"type":"statement","id":"Q41050$06B30AD3-E636-425F-A7E1-16D82FFA479B","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"c38c62ee935208dd7e0a311f58eb2f882ae7e0de","datavalue":{"value":"CID11:8B60.6","type":"string"},"datatype":"string"},"type":"statement","id":"Q41050$A7C9085E-AA58-405B-8244-0CF510144B05","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"cc29567098c28d3ac91092f2fc2905568656155b","datavalue":{"value":"dki-india-8B60.6","type":"string"},"datatype":"string"},"type":"statement","id":"Q41050$79879632-24F1-486E-AAF1-28C0FA5B9F9F","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q41050$0F49A4AB-6A59-4A39-A641-B64F1C4498DF","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q41050$AF30BBF2-B979-4684-8FE9-C14358ADFCF6","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q41050$3C55CD25-EF3E-4BB7-8604-CE3EC9DB949B","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"ea31a01f219e449243632e6aea5d14e92c40b2c6","datavalue":{"value":{"entity-type":"item","numeric-id":16832,"id":"Q16832"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q41050$8E0CA34D-88E3-4689-B536-A9F7B46EEA3E","rank":"normal"}]},"sitelinks":{}}}}