{"entities":{"Q41045":{"pageid":31413,"ns":120,"title":"Item:Q41045","lastrevid":134877,"modified":"2026-08-13T07:05:54Z","type":"item","id":"Q41045","labels":{"mul":{"language":"mul","value":"8B61.2"},"pt-br":{"language":"pt-br","value":"Distrofia muscular espinal forma juvenil, tipo III"},"en":{"language":"en","value":"Juvenile form spinal muscular dystrophy, Type III"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Na AMS tipo 3, a fraqueza dos m\u00fasculos \u00e9 observada ap\u00f3s os 18 meses de idade. A crian\u00e7a consegue sentar-se e ficar em p\u00e9 de forma independente. H\u00e1 uma distribui\u00e7\u00e3o de fraqueza do tipo cintura-membros, causando marcha cambaleante, quedas e dificuldade para correr. A capacidade de andar pode ser perdida, exigindo uma cadeira de rodas \u00e0 medida que a doen\u00e7a progride. A expectativa de vida pode ser normal."},"en":{"language":"en","value":"In SMA type 3, weakness of muscles is seen after 18 months of age. The child is able to sit and stand independently. There is a limb girdle-type of distribution of weakness causing waddling gait, falls, and difficulty with running. The ability to walk may be lost, requiring a wheelchair as the disease progresses. The life expectancy may be normal."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"2f60926ca4ea60b6231ad64bbcfdf95284627658","datavalue":{"value":"https://id.who.int/icd/entity/677572815","type":"string"},"datatype":"url"},"type":"statement","id":"Q41045$B01CAC6F-C52C-4677-9E41-4EF70313320C","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"2da707117025e60678b73545d6f0bc85646a9d07","datavalue":{"value":"CID11:8B61.2","type":"string"},"datatype":"string"},"type":"statement","id":"Q41045$2F17D5BD-3EF9-466B-8524-684ABF95AC15","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"3feecd9844149b2fe842ba247390ae9d4dc43be9","datavalue":{"value":"dki-india-8B61.2","type":"string"},"datatype":"string"},"type":"statement","id":"Q41045$D06DB76C-E6AC-4524-9765-0147C1AE4523","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q41045$4AAA987B-CFC5-423C-AA2B-0C0090A3AEE0","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q41045$D2698A80-40BE-4F2E-8669-BB703A7B7891","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q41045$0746CC8C-85ED-4FE2-9B8C-BE5D7792EB2C","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"daa6746ced56658902542ddc1a87f5dcc6588e17","datavalue":{"value":{"entity-type":"item","numeric-id":16826,"id":"Q16826"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q41045$E7F48D4A-B0E7-408A-8340-7341DDC91659","rank":"normal"}]},"sitelinks":{}}}}