{"entities":{"Q39613":{"pageid":29981,"ns":120,"title":"Item:Q39613","lastrevid":122246,"modified":"2026-08-13T05:05:48Z","type":"item","id":"Q39613","labels":{"mul":{"language":"mul","value":"3B62.4"},"pt-br":{"language":"pt-br","value":"defici\u00eancia de gr\u00e2nulos densos alfa delta"},"en":{"language":"en","value":"Alpha-delta dense granule deficiency"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Condi\u00e7\u00e3o causada por determinantes que surgem ap\u00f3s o nascimento, no per\u00edodo neonatal. Esta condi\u00e7\u00e3o \u00e9 caracterizada por defeitos nos gr\u00e2nulos densos alfa delta das plaquetas, levando a anormalidades nos mecanismos de coagula\u00e7\u00e3o. Esta condi\u00e7\u00e3o pode se apresentar com sangramento prolongado, epistaxe, menorragia, hematomas frequentes, anemia, fadiga e falta de ar. A confirma\u00e7\u00e3o \u00e9 pela identifica\u00e7\u00e3o dos baixos n\u00edveis de gr\u00e2nulos densos alfa delta em amostra do sangue."},"en":{"language":"en","value":"A condition caused by determinants arising after birth, in the antenatal period. This condition is characterised by defects in the alpha delta dense granules in platelets, leading to abnormalities in coagulation mechanisms. This condition may present with prolonged bleeding, epistaxis, menorrhagia, easy bruising, anaemia, fatigue or shortness of breath. Confirmation is by identification of low levels of alpha delta dense granules in a blood sample."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"163991532da0964551882da18328d196f3ab1223","datavalue":{"value":"https://id.who.int/icd/entity/1557840180","type":"string"},"datatype":"url"},"type":"statement","id":"Q39613$B3F2F5DE-A214-45D1-8595-33026322F8F2","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"e9a9612c5115ba56ea1587e9ee55d9077693e5b3","datavalue":{"value":"CID11:3B62.4","type":"string"},"datatype":"string"},"type":"statement","id":"Q39613$9569FAD8-B60B-4237-ABD3-E44C0F0943EE","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"eae4501244ea6c8875e46e3b6b7425cafacaa430","datavalue":{"value":"dki-india-3B62.4","type":"string"},"datatype":"string"},"type":"statement","id":"Q39613$FE1DD3EB-334B-405A-B605-43DC26DF54C0","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q39613$95E07A5C-F541-42D7-ADEA-D85A269D445C","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q39613$BEAFCAF5-2A35-4E93-8810-710270383D84","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q39613$75140E46-952C-47FC-B2B8-B8C6C37ADC6E","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"e0bb6896086d796718147528d7cad6569a80c6bd","datavalue":{"value":{"entity-type":"item","numeric-id":14794,"id":"Q14794"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q39613$3253DA21-51AD-4008-AC1C-4C55E80F4435","rank":"normal"}]},"sitelinks":{}}}}