{"entities":{"Q39607":{"pageid":29973,"ns":120,"title":"Item:Q39607","lastrevid":122196,"modified":"2026-08-13T05:05:22Z","type":"item","id":"Q39607","labels":{"mul":{"language":"mul","value":"3B50.1"},"pt-br":{"language":"pt-br","value":"Defici\u00eancia cong\u00eanita do inibidor do ativador do plasminog\u00eanio tecidual tipo 1"},"en":{"language":"en","value":"Congenital plasminogen activator inhibitor type 1 deficiency"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A defici\u00eancia cong\u00eanita do inibidor do ativador do plasminog\u00eanio tecidual tipo 1 (PAI-1) \u00e9 um transtorno que causa lise prematura de co\u00e1gulos hemost\u00e1ticos e uma s\u00edndrome hemorr\u00e1gica moderada. Sangramento espont\u00e2neo \u00e9 raramente observado, enquanto hemorragias moderadas nos joelhos, cotovelos, nariz e gengiva s\u00e3o habitualmente desencadeadas por trauma leve. Entretanto, o sangramento menstrual pode ser grave, e um sangramento prolongado ap\u00f3s cirurgia \u00e9 comum. A defici\u00eancia do PAI-1 pode ser qualitativa ou quantitativa, total ou parcial."},"en":{"language":"en","value":"Congenital plasminogen activator inhibitor type 1 (PAI-1) deficiency is a disorder that causes premature lysis of haemostatic clots and a moderate bleeding syndrome. Spontaneous bleeding is rarely observed, whereas moderate haemorrhages of the knees, elbows, nose and gingiva are usually triggered by mild trauma. However, menstrual bleeding may be severe and a prolonged bleeding after surgery is common. The PAI-1 deficiency may be qualitative or quantitative, total or partial."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"101bb7dada5bc06e740301db4127ed57edde729c","datavalue":{"value":"https://id.who.int/icd/entity/428643962","type":"string"},"datatype":"url"},"type":"statement","id":"Q39607$DF53A2B7-0B24-4620-9DE2-DD46511E3015","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"20826d84e7ba1179fee49ea24679b64cf164716b","datavalue":{"value":"CID11:3B50.1","type":"string"},"datatype":"string"},"type":"statement","id":"Q39607$2DEB3807-9D0B-42E7-8503-293B3DBB4585","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"ad496324db1cc842bfdd8dc47a15ed1533d3785d","datavalue":{"value":"dki-india-3B50.1","type":"string"},"datatype":"string"},"type":"statement","id":"Q39607$A456E442-D9E9-4B7E-BE03-5EC3BC934FE8","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q39607$2A693817-0D42-4041-B8F4-027845839B41","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q39607$8AEABB5F-A926-49A8-9B5B-A2947FB955E0","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q39607$4918813E-152F-4208-97BC-AEA1202E97F5","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"cba759ef0ffff7bb346d04b169eeed444386a32d","datavalue":{"value":{"entity-type":"item","numeric-id":14785,"id":"Q14785"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q39607$9AC90237-38DC-4660-8F43-14521963BEAC","rank":"normal"}]},"sitelinks":{}}}}