{"entities":{"Q39573":{"pageid":29939,"ns":120,"title":"Item:Q39573","lastrevid":121951,"modified":"2026-08-13T05:03:06Z","type":"item","id":"Q39573","labels":{"mul":{"language":"mul","value":"3B10.1"},"pt-br":{"language":"pt-br","value":"Defici\u00eancia heredit\u00e1ria do fator VIII com inibidor anti-fator VIII"},"en":{"language":"en","value":"Hereditary factor VIII deficiency with anti-factor VIII inhibitor"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Doen\u00e7a causada por uma muta\u00e7\u00e3o geneticamente herdada levando a uma defici\u00eancia na coagula\u00e7\u00e3o devido \u00e0 falta de fator VIII. Essa doen\u00e7a tamb\u00e9m causa a produ\u00e7\u00e3o de anticorpos inibidores antifator VIII quando do recebimento de transfus\u00f5es. Anticorpos inibidores antifator VIII desenvolvem-se diante do reconhecimento do fator VIII como estranho pelo organismo, o que resulta na inefic\u00e1cia de infus\u00f5es de fator VIII. Essa doen\u00e7a \u00e9 caracterizada pelo aumento na ocorr\u00eancia de hemorragias e equimoses. A confirma\u00e7\u00e3o \u00e9 feita pela identifica\u00e7\u00e3o de muta\u00e7\u00f5es por testagem gen\u00e9tica."},"en":{"language":"en","value":"A disease caused by a genetically inherited mutation leading to a deficiency in clotting due to lack of factor VIII. This disease also causes anti-factor VIII inhibitor antibodies to be produced when receiving transfusions. Anti-factor VIII inhibitor antibodies develop as the body recognises the factor VIII as foreign, therefore deeming factor VIII infusions ineffective. This disease is characterised by increasing haemorrhaging and bruising. Confirmation is by identification of mutations by genetic testing."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"36693060d877e1b53d7113017aaf605006688c86","datavalue":{"value":"https://id.who.int/icd/entity/765707742","type":"string"},"datatype":"url"},"type":"statement","id":"Q39573$EE4CFBAA-D19C-40CB-B93E-DA5CBDE96111","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"dc7509035128ff847002a4f01e15ed73536c99ca","datavalue":{"value":"CID11:3B10.1","type":"string"},"datatype":"string"},"type":"statement","id":"Q39573$880EC7DA-B992-43DE-A1FC-E2861C97B93D","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"99a550e96c064c24725bfd7aaad69450624a58cd","datavalue":{"value":"dki-india-3B10.1","type":"string"},"datatype":"string"},"type":"statement","id":"Q39573$610FB254-2DBB-40B7-A79F-56E720C23E8E","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q39573$9EAF98EE-D200-496C-BB78-C77B1809F24D","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q39573$90CC1B85-0546-4474-935A-C9857F49241B","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q39573$DF195F89-E2B5-4042-8C19-4BBA6CF79D02","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"86bdbb1a0d876d299dbd041f7cd412be503587f9","datavalue":{"value":{"entity-type":"item","numeric-id":14770,"id":"Q14770"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q39573$5466CB06-53DB-4016-A510-51746CDEE761","rank":"normal"}]},"sitelinks":{}}}}