{"entities":{"Q39522":{"pageid":29888,"ns":120,"title":"Item:Q39522","lastrevid":121470,"modified":"2026-08-13T04:58:18Z","type":"item","id":"Q39522","labels":{"mul":{"language":"mul","value":"3A51.A"},"pt-br":{"language":"pt-br","value":"Doen\u00e7a da hemoglobina E"},"en":{"language":"en","value":"Haemoglobin E disease"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Doen\u00e7a da hemoglobina E \u00e9 caracterizada pela s\u00edntese de uma hemoglobina anormal chamada hemoglobina E (Hb E), em vez da hemoglobina A normal (Hb A). Indiv\u00edduos heterozigotos para Hb E (AE) t\u00eam uma condi\u00e7\u00e3o assintom\u00e1tica sem relev\u00e2ncia cl\u00ednica, exceto pelo risco de transmitir talassemia E/beta talassemia se o outro progenitor for portador da beta talassemia. A gravidade destas formas de E/beta talassemia \u00e9 muito vari\u00e1vel, e o quadro cl\u00ednico varia daquela do tra\u00e7o da talassemia minor at\u00e9 talassemia interm\u00e9dia e talassemia maior. Os indiv\u00edduos homozigotos para Hb E (EE) s\u00e3o assintom\u00e1ticos."},"en":{"language":"en","value":"Haemoglobin E disease is characterised by the synthesis of an abnormal haemoglobin called haemoglobin E (HbE), instead of the normal haemoglobin A (HbA). Subjects heterozygous for HbE (AE) have an asymptomatic condition with no clinical relevance, except for the risk of transmitting E/beta thalassemia if the other parent carries beta thalassemia. The severity of these E/beta thalassemia forms is very variable, the clinical picture ranging from that of beta thalassemia minor through to thalassemia intermedia to thalassemia major. Subjects homozygous for HbE (EE) are asymptomatic."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"42da8b0b245b3d55aff868cb777dcae1687bc51f","datavalue":{"value":"https://id.who.int/icd/entity/1898135714","type":"string"},"datatype":"url"},"type":"statement","id":"Q39522$22AC7174-84B2-45E9-869E-2305308BE078","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"b2308c0359d21ede90cd265ca0f48376be045aa6","datavalue":{"value":"CID11:3A51.A","type":"string"},"datatype":"string"},"type":"statement","id":"Q39522$811533EE-21E2-4D4A-865C-588AD60A2BFB","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"3696bbf3af27f87903d640597b434b68874084cf","datavalue":{"value":"dki-india-3A51.A","type":"string"},"datatype":"string"},"type":"statement","id":"Q39522$31A208B0-F2A4-445B-83C0-AA16C06B1010","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q39522$3650332E-0DF0-4365-8316-37EC5EC53632","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q39522$68381C3E-0D92-45BA-8E5D-388BEA324A95","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"92b8222fcbb75718504f915073a3f43bd4003d18","datavalue":{"value":{"time":"+2026-08-13T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q39522$45A8CB47-680D-48F3-B0B8-9AF9176C252A","rank":"normal"}],"P89":[{"mainsnak":{"snaktype":"value","property":"P89","hash":"405b00f4994c05f6c25ec050288d6b0eb686e9e5","datavalue":{"value":{"entity-type":"item","numeric-id":14676,"id":"Q14676"},"type":"wikibase-entityid"},"datatype":"wikibase-item"},"type":"statement","id":"Q39522$C5D75000-4CD0-4D10-911B-A6C30EC00F0C","rank":"normal"}]},"sitelinks":{}}}}