{"entities":{"Q104667":{"pageid":95065,"ns":120,"title":"Item:Q104667","lastrevid":603658,"modified":"2026-08-17T10:32:08Z","type":"item","id":"Q104667","labels":{"mul":{"language":"mul","value":"ID_995395080"},"pt-br":{"language":"pt-br","value":"Doen\u00e7a de Charcot-Marie-Thooth tipo 4G"},"en":{"language":"en","value":"Charcot-Marie-Tooth disease type 4G"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A doen\u00e7a de Charcot-Marie-Tooth tipo 4G (CMT4G) \u00e9 uma polineuropatia perif\u00e9rica sensitivomotora da CMT desmielinizante identificada em ciganos b\u00falgaros, romenos, franceses e espanh\u00f3is e que tamb\u00e9m \u00e9 conhecida como neuropatia motora e sensorial heredit\u00e1ria-Russe (HMSNR). O in\u00edcio ocorre entre 8 e 16 anos de idade com fraqueza distal dos membros inferiores, seguida por envolvimento distal dos membros superiores com uma idade de in\u00edcio mais vari\u00e1vel entre 10 e 43 anos. A perda sensitiva tamb\u00e9m \u00e9 uma caracter\u00edstica proeminente."},"en":{"language":"en","value":"Charcot-Marie-Tooth disease, type 4G (CMT4G) is a demyelinating CMT peripheral sensorimotor polyneuropathy identified in Bulgarian, Romanian, French, and Spanish Gypsies and is also referred to as hereditary motor and sensory neuropathy-Russe (HMSNR). Onset occurs between 8 and 16 years of age with distal lower limb weakness, followed by distal upper limb involvement with a more variable age of onset of between 10 and 43 years. Sensory loss is also a prominent feature."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"3fa7ceb6934dac7110ab516a17f1f24587bc5c2b","datavalue":{"value":"https://id.who.int/icd/entity/995395080","type":"string"},"datatype":"url"},"type":"statement","id":"Q104667$99E135A7-1CBE-4D53-85D4-DEBD526232E5","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"fbe1701b0eb4203def8c7f98ef9d5413b7f6ea96","datavalue":{"value":"CID11:ID_995395080","type":"string"},"datatype":"string"},"type":"statement","id":"Q104667$691CFDCC-5EDB-4A33-915B-CE5B7978E84C","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"c55227d54fa623001d1db2c0741a0512db0feb27","datavalue":{"value":"dki-india-ID_995395080","type":"string"},"datatype":"string"},"type":"statement","id":"Q104667$6D0BAC32-1514-4E9A-9714-374A7752D77E","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q104667$8CDF71B4-72F5-40D8-94F8-5FDFC8CFDFD8","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q104667$08634569-1B50-4CB3-AAA3-C46BE29A0F28","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"8612011b2ca718e4ec0db5a49d2de6d25b2e811c","datavalue":{"value":{"time":"+2026-08-16T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q104667$7BF23DC5-6006-4A8C-9C55-C972B9AF0D89","rank":"normal"}]},"sitelinks":{}}}}