{"entities":{"Q103466":{"pageid":93864,"ns":120,"title":"Item:Q103466","lastrevid":594984,"modified":"2026-08-17T09:13:49Z","type":"item","id":"Q103466","labels":{"mul":{"language":"mul","value":"ID_1034981351"},"pt-br":{"language":"pt-br","value":"Atividade cont\u00ednua da fibra muscular heredit\u00e1ria"},"en":{"language":"en","value":"Hereditary continuous muscle fibre activity"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A hiperexcitabilidade do nervo perif\u00e9rico generelizada \u00e9 um grupo heterog\u00eaneo de dist\u00farbios que se apresentam como hiperatividade muscular cont\u00ednua e involunt\u00e1ria. A apresenta\u00e7\u00e3o cl\u00ednica pode incluir c\u00e3ibras musculares, fascicula\u00e7\u00f5es, mioquimia (movimentos ondulantes da superf\u00edcie da pele) e pseudomiotonia (relaxamento retardado ap\u00f3s uma contra\u00e7\u00e3o). Existem muitas s\u00edndromes de hiperexcitabilidade de nervos perif\u00e9ricos, com patog\u00eanese diferente que inclui dist\u00farbios gen\u00e9ticos e adquiridos. A mais conhecida \u00e9 a s\u00edndrome de Isaacs, frequentemente chamada de neuromiotonia adquirida."},"en":{"language":"en","value":"Generalised peripheral nerve hyperexcitability are a heterogeneous group of disorders presenting as involuntary, continuous muscle overactivity. The clinical presentation can include muscle cramps, fasciculations, myokymia (undulating movements of the skin surface), and pseudomyotonia (delayed relaxation after a contraction). There are many peripheral nerve hyperexcitability syndromes, with different pathogenesis that include both genetic and acquired disorders. The most well-known is Isaacs syndrome, often called acquired neuromyotonia."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"a240431d0c6d3d07db2ecf41aa1fc58d69a8a166","datavalue":{"value":"https://id.who.int/icd/entity/1034981351","type":"string"},"datatype":"url"},"type":"statement","id":"Q103466$7DC5445C-17CE-488B-8212-FBCA6A64F571","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"ac54cabc2864b0949f379f220a6bbcffb0204df5","datavalue":{"value":"CID11:ID_1034981351","type":"string"},"datatype":"string"},"type":"statement","id":"Q103466$0973C252-3E30-4EAA-938D-25D48A2E3D61","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"7fe5d18ac8210834e3cea9c92392aee593714797","datavalue":{"value":"dki-india-ID_1034981351","type":"string"},"datatype":"string"},"type":"statement","id":"Q103466$B419E257-9945-4880-B610-D3342F352C48","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q103466$EEFF5293-9CCC-4F95-881F-FD5988AF745A","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q103466$24F6C514-36A5-4B74-83AF-6BD5F621132B","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"8612011b2ca718e4ec0db5a49d2de6d25b2e811c","datavalue":{"value":{"time":"+2026-08-16T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q103466$9B84EC4E-5D4B-4D7A-BBAD-963B5A5B7C0F","rank":"normal"}]},"sitelinks":{}}}}