{"entities":{"Q102736":{"pageid":93129,"ns":120,"title":"Item:Q102736","lastrevid":589679,"modified":"2026-08-16T19:56:58Z","type":"item","id":"Q102736","labels":{"mul":{"language":"mul","value":"ID_1572086295"},"pt-br":{"language":"pt-br","value":"Citrulinemia tipo 2"},"en":{"language":"en","value":"Citrullinaemia type 2"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Citrulinemia tipo 2 \u00e9 um subtipo grave de defici\u00eancia de citrina caracterizada clinicamente por in\u00edcio na vida adulta (entre 20 e 50 anos de idade), epis\u00f3dios recorrentes de hiperamonemia e sintomas neuropsiqui\u00e1tricos associados, como del\u00edrio noturno, confus\u00e3o, inquieta\u00e7\u00e3o, desorienta\u00e7\u00e3o, sonol\u00eancia, perda de mem\u00f3ria, comportamento anormal (agress\u00e3o, irritabilidade e hiperatividade), convuls\u00f5es e coma."},"en":{"language":"en","value":"Citrullinemia type 2 is a severe subtype of citrin deficiency characterised clinically by adult onset (20 and 50 years of age), recurrent episodes of hyperammonemia and associated neuropsychiatric symptoms such as nocturnal delirium, confusion, restlessness, disorientation, drowsiness, memory loss, abnormal behaviour (aggression, irritability, and hyperactivity), seizures, and coma."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"b2fd197b6d5613fce92ccf65de8c4f3247c40deb","datavalue":{"value":"https://id.who.int/icd/entity/1572086295","type":"string"},"datatype":"url"},"type":"statement","id":"Q102736$7CAE0861-34F2-493D-831E-3B73B0E9DAB5","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"66e31900471161a1f9630f9963b878caf33b21b3","datavalue":{"value":"CID11:ID_1572086295","type":"string"},"datatype":"string"},"type":"statement","id":"Q102736$73CFE1C0-B00E-48CA-93A3-46DF6700CEE3","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"efb0e88c7f07d374810b12550136a049a9bdd7bc","datavalue":{"value":"dki-india-ID_1572086295","type":"string"},"datatype":"string"},"type":"statement","id":"Q102736$098CF8C4-6370-46EB-A804-5FE5FF6F2AAD","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q102736$A5BDCED2-CF03-42AF-A388-24C16C863AD9","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q102736$5EB8C9C6-2A11-4BD1-99B3-F5337A46014F","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q102736$A0BB4F46-95A7-4C51-893E-7C2D8EB93264","rank":"normal"}]},"sitelinks":{}}}}