{"entities":{"Q101273":{"pageid":91666,"ns":120,"title":"Item:Q101273","lastrevid":579084,"modified":"2026-08-16T18:04:36Z","type":"item","id":"Q101273","labels":{"mul":{"language":"mul","value":"ID_1844018161"},"pt-br":{"language":"pt-br","value":"Miopatia distal, tipo Miyoshi"},"en":{"language":"en","value":"Distal myopathy, Miyoshi type"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A miopatia de Miyoshi (disferlinopatia) pertence ao grupo heterog\u00eaneo de miopatias distais e \u00e9 clinicamente caracterizada por fraqueza e atrofia das panturrilhas, que \u00e0s vezes \u00e9 assim\u00e9trica, levando \u00e0 incapacidade de pular, correr ou andar na ponta dos p\u00e9s, e que subsequentemente progride para a parte superior e membros inferiores. Os m\u00fasculos faciais, bulbares e card\u00edacos s\u00e3o poupados."},"en":{"language":"en","value":"Miyoshi myopathy (dysferlinopathy) belongs to the heterogeneous group of distal myopathies, and is clinically characterised by weakness and atrophy of the calves, which is sometimes asymmetrical, leading to inability to jump, run or walk on tiptoes, and that subsequently progresses to the upper and lower limbs. Facial, bulbar and cardiac muscles are spared."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"485a5b907de4f354dc0f657502bf112a3f9fcc17","datavalue":{"value":"https://id.who.int/icd/entity/1844018161","type":"string"},"datatype":"url"},"type":"statement","id":"Q101273$A31CC8AE-20A8-4EA7-9430-EFE37EB3C06A","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"9581b7d38e5ef371e6e37a0e81702a019cd15a0d","datavalue":{"value":"CID11:ID_1844018161","type":"string"},"datatype":"string"},"type":"statement","id":"Q101273$B47B7AFF-EF14-4569-B9F2-C6BA4F8E46D1","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"c5ef519e22cc7f485d0cfdf09325ee2c3f1cd2c6","datavalue":{"value":"dki-india-ID_1844018161","type":"string"},"datatype":"string"},"type":"statement","id":"Q101273$F4501AC7-D8CC-405C-9E05-D136C1A1955B","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q101273$C90CDD61-84F3-4AAE-902F-A500A1934B97","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q101273$1FDFB804-A5A8-40E3-8377-73F92AF7CBDE","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q101273$7294F083-D380-4A72-89AF-C2E12B8189E4","rank":"normal"}]},"sitelinks":{}}}}