{"entities":{"Q101018":{"pageid":91411,"ns":120,"title":"Item:Q101018","lastrevid":577220,"modified":"2026-08-16T17:48:27Z","type":"item","id":"Q101018","labels":{"mul":{"language":"mul","value":"ID_1275925881"},"pt-br":{"language":"pt-br","value":"Ganglionopatia sensitiva autoimune, autoanticorpo neuronal positivo"},"en":{"language":"en","value":"Autoimmune sensory ganglionopathy, neural autoantibody positive"}},"descriptions":{"pt-br":{"language":"pt-br","value":"A ganglionopatia sensitiva autoimune ocorre como neuropatia sensitiva aguda, em associa\u00e7\u00e3o com a s\u00edndrome de Sj\u00f6gren tamb\u00e9m pansenssitiva, pequenas fibras , CANVAS (Ataxia cerebelar, neuropatia, s\u00edndrome de arreflexia vestibular), condi\u00e7\u00f5es t\u00f3xicas como intoxica\u00e7\u00e3o por piridoxina e tamb\u00e9m tratamento com cisplatina devem ser considerados._x000D_ Tem um in\u00edcio subagudo, perda sensorial grave resultando em ataxia. O in\u00edcio pode ser assim\u00e9trico, geralmente come\u00e7ando nos bra\u00e7os e associado \u00e0 dor neurop\u00e1tica. Uma vez estabelecido, tem curso cr\u00f4nico e ininterrupto, incapacitando o paciente. Anticorpo positivo: os perfis de anticorpos s\u00e3o atualmente desconhecidos."},"en":{"language":"en","value":"Autoimmune sensory ganglionopathy occurs as acute sensory neuropathy, in association with Sj\u00f6gren`s syndrome also pansensory, small fibre, CANVAS (Cerebellar Ataxia, neuropathy, vestibular areflexia syndrome, toxic conditions as pyridoxin intoxication and also cis platinum treatment must be considered. It has a subacute onset, severe sensory loss resulting in ataxia. The onset can be asymmetric, often beginning in the arms and associated with neuropathic pain. Once established it has a chronic and unremitting course disabling the patient. Antibody positive: Antibody profiles are currently unknown."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"3f0e9cc19192964f2a442d92175acb8bea2a1c18","datavalue":{"value":"https://id.who.int/icd/entity/1275925881","type":"string"},"datatype":"url"},"type":"statement","id":"Q101018$4D71AF3E-ED36-422E-B834-1FA0C9808551","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"07e441bd6aa46b3cc4cf948d5f0554b61581c6b5","datavalue":{"value":"CID11:ID_1275925881","type":"string"},"datatype":"string"},"type":"statement","id":"Q101018$F0323BCF-C7C7-4E67-991C-34951DFEA8A8","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"41160c8ec3cec0d9ed863cb5724df6d0a93e1eaf","datavalue":{"value":"dki-india-ID_1275925881","type":"string"},"datatype":"string"},"type":"statement","id":"Q101018$7FFF86B1-9B5E-4B99-BEAC-5506C8A06845","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q101018$B9A85316-D698-412D-9853-612ADE6EFD39","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q101018$C696B436-F12F-4623-B949-E6458C87E107","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q101018$5A6A6C22-DDAE-4F08-A349-ABF6C4E05363","rank":"normal"}]},"sitelinks":{}}}}