{"entities":{"Q100609":{"pageid":91002,"ns":120,"title":"Item:Q100609","lastrevid":574230,"modified":"2026-08-16T17:20:27Z","type":"item","id":"Q100609","labels":{"mul":{"language":"mul","value":"ID_288209958"},"pt-br":{"language":"pt-br","value":"S\u00edndrome da pessoa r\u00edgida, forma variante"},"en":{"language":"en","value":"Stiff person syndrome variant form"}},"descriptions":{"pt-br":{"language":"pt-br","value":"V\u00e1rias formas variantes da s\u00edndrome da pessoa r\u00edgida podem ocorrer como um fen\u00f4meno autoimune sem c\u00e2ncer ou como um transtorno autoimune paraneopl\u00e1sico. Os principais subtipos incluem membro r\u00edgido (envolvendo apenas uma extremidade), tronco r\u00edgido (isolada ao tronco) e encefalomielite progressiva com rigidez e mioclonia (uma apresenta\u00e7\u00e3o mais grave envolvendo m\u00faltiplas facetas do sistema nervoso). Semelhante \u00e0 s\u00edndrome da pessoa r\u00edgida cl\u00e1ssica [ver s\u00edndrome da pessoa r\u00edgida cl\u00e1ssica], eles geralmente s\u00e3o acompanhados por autoanticorpos GAD65, mas outros autoanticorpos neurais podem ser encontrados."},"en":{"language":"en","value":"A number of variant forms of stiff person syndrome may occur as an autoimmune phenomenon without cancer or as a paraneoplastic autoimmune disorder. The major subtypes include stiff limb (involving only one extremity), stiff trunk (isolated to the trunk) and progressive encephalomyelitis rigidity and myoclonus (a more severe presentation involving multiple facets of the nervous system). Similar to classic stiff person syndrome [see classic stiff person syndrome] they are often accompanied by GAD65 autoantibodies but other neural autoantibodies may be found."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"f5c417e8a5f6a3ae2a1cb48b87577853bf54020f","datavalue":{"value":"https://id.who.int/icd/entity/288209958","type":"string"},"datatype":"url"},"type":"statement","id":"Q100609$64124965-61F5-43E0-BE06-C4B2FAA78B5B","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"c78cdc4ca836dcf577711d66fb8a4716e0502b18","datavalue":{"value":"CID11:ID_288209958","type":"string"},"datatype":"string"},"type":"statement","id":"Q100609$D04F27ED-4557-41A8-A906-F1FCDCE9083A","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"6a7a1bea2fed4ece9c3a3bbc30d2fb462407b161","datavalue":{"value":"dki-india-ID_288209958","type":"string"},"datatype":"string"},"type":"statement","id":"Q100609$63CD2599-1570-407A-B20D-4447704BA1D9","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q100609$7F7E1806-EF18-4EE4-9677-00230DE766E0","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q100609$39C028F8-A031-4B49-80B5-B689EC18C889","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q100609$86AE3B03-A95E-4EAA-B33E-DB321FF52199","rank":"normal"}]},"sitelinks":{}}}}