{"entities":{"Q100280":{"pageid":90673,"ns":120,"title":"Item:Q100280","lastrevid":571868,"modified":"2026-08-16T16:59:17Z","type":"item","id":"Q100280","labels":{"mul":{"language":"mul","value":"ID_458884245"},"pt-br":{"language":"pt-br","value":"\u00cdleo meconial na fibrose c\u00edstica at\u00edpica"},"en":{"language":"en","value":"Meconium ileus in atypical cystic fibrosis"}},"descriptions":{"pt-br":{"language":"pt-br","value":"Ocorre quando o mec\u00f4nio se torna espesso e congestiona o \u00edleo, em uma doen\u00e7a gen\u00e9tica autoss\u00f4mica recessiva at\u00edpica que afeta principalmente os pulm\u00f5es, mas tamb\u00e9m p\u00e2ncreas, f\u00edgado e intestino. Caracteriza-se pelo transporte anormal de cloretos e s\u00f3dio atrav\u00e9s de um epit\u00e9lio, levando \u00e0 produ\u00e7\u00e3o de secre\u00e7\u00f5es espessas e viscosas."},"en":{"language":"en","value":"This is where the meconium sometimes becomes thickened and congested in the ileum, in an atypical autosomal recessive genetic disorder that affects most critically the lungs, and also the pancreas, liver, and intestine. It is characterised by abnormal transport of chloride and sodium across an epithelium, leading to thick, viscous secretions."}},"aliases":{},"claims":{"P68":[{"mainsnak":{"snaktype":"value","property":"P68","hash":"25cd840315e9ccedcb1e49c5b5f8bb275f9b355b","datavalue":{"value":"https://id.who.int/icd/entity/458884245","type":"string"},"datatype":"url"},"type":"statement","id":"Q100280$905D5723-8325-44C6-B6DC-2ECECBE8EE2C","rank":"normal"}],"P67":[{"mainsnak":{"snaktype":"value","property":"P67","hash":"e7d9777053854cf5c22b63d3d47502eb43e1f6ba","datavalue":{"value":"CID11:ID_458884245","type":"string"},"datatype":"string"},"type":"statement","id":"Q100280$4A502311-4DF3-4F81-B520-DD3F5E91B331","rank":"normal"}],"P70":[{"mainsnak":{"snaktype":"value","property":"P70","hash":"6a578e7419d517888a93198c98ebc215b77f391e","datavalue":{"value":"dki-india-ID_458884245","type":"string"},"datatype":"string"},"type":"statement","id":"Q100280$DB9359CD-AAFC-4943-B6EC-A32F5112CF93","rank":"normal"}],"P86":[{"mainsnak":{"snaktype":"value","property":"P86","hash":"a96031634b9f5dafddaf781bbba3adea6bb64ef4","datavalue":{"value":"Conclu\u00eddo","type":"string"},"datatype":"string"},"type":"statement","id":"Q100280$AF072A07-6CFC-48A3-88F1-CCB9D4E3DBED","rank":"normal"}],"P78":[{"mainsnak":{"snaktype":"value","property":"P78","hash":"5f9b5be68b7400da549761cf15abfdbc4d1e075b","datavalue":{"value":"https://pauloleads.com.br/cases-publicos/","type":"string"},"datatype":"url"},"type":"statement","id":"Q100280$53284C66-99D3-4A99-B680-9F7C63645EB9","rank":"normal"}],"P80":[{"mainsnak":{"snaktype":"value","property":"P80","hash":"378ac503ed43f21e1f461d2823a6ad59da580514","datavalue":{"value":{"time":"+2026-08-15T00:00:00Z","timezone":0,"before":0,"after":0,"precision":11,"calendarmodel":"http://www.wikidata.org/entity/Q1985727"},"type":"time"},"datatype":"time"},"type":"statement","id":"Q100280$F5F2D551-3F68-4155-85DE-37538EB27BCF","rank":"normal"}]},"sitelinks":{}}}}